Inborn Errors of Metabolism(先天性代谢缺陷病)

Cat.No. 产品名称 Information

GC43758 Globotriaosylceramides (hydroxy) (porcine) Globotriaosycleramides are glycosphingolipids found in mammalian cell membranes that are synthesized from lactosylceramides.

GC43727 Ganglioside GD1a mixture (sodium salt) A mixture of ganglioside G_D1a

GC43723 Galactosylsphingosine (d18:1) A bioactive sphingolipid

GC43722 Galactosylcerebrosides (non-hydroxy) A sphingolipid

GC43721 Galactosylcerebrosides (hydroxy) A mixture of isolated bovine hydroxy galactosylceramides

GC43068 C20 Sphingomyelin (d18:1/20:0) A sphingolipid

GC43059 C2 Adamantanyl Galactosylceramide (d18:1/2:0) C2 金刚烷基半乳糖神经酰胺 (d18:1/2:0) (AdaGalCer) 是一种具有生物活性的鞘脂。

GC43049 C18 Globotriaosylceramide (d18:1/18:0) A sphingolipid

GC43041 C17 Globotriaosylceramide (d18:1/17:0) A sphingolipid

GC43038 C17 Ceramide (d18:1/17:0) A synthetic ceramide

GC43035 C16 Sphingomyelin (d18:1/16:0) A sphingolipid

GC43033 C16 Lactosylceramide (d18:1/16:0) A bioactive sphingolipid

GC43032 C16 Globotriaosylceramide (d18:1/16:0) A sphingolipid

GC43006 C12 Ceramide (d18:1/12:0) A naturally occurring ceramide

GC42963 BODIPY-C12 Ceramide (d18:1/12:0) A fluorescently-tagged C12 ceramide

GC42695 Acetoacetyl Coenzyme A (sodium salt hydrate) A precursor to HMG-CoA

GC42445 4-Methylumbelliferyl β-D-Galactopyranoside-6-sulfate (sodium salt) A fluorogenic substrate of GALNS

GC42442 4-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (sodium salt) A fluorogenic substrate of heparin sulphamidase

GC42292 3-Hydroxypropionic Acid (sodium salt) A building block in the synthesis of a variety of compounds

GC42051 1-β-D-Glucosylsphingosine (d18:1) A lysolipid derivative of glucocerebroside

GC41907 13C C16 Sphingomyelin (d18:1/16:0) An internal standard for the quantification of C16 sphingomyelin

GC41614 24-dehydro Cholesterol An immediate precursor of cholesterol

GC41582 4(Z),7(Z)-Decadienoic Acid A PUFA

GC40510 4-Methylumbelliferyl-α-D-Galactopyranoside A fluorogenic substrate of α-galactosidase

GC40341 Tetrahydro-11-deoxy Cortisol A metabolite of 11-deoxycortisol

GC11870 4-Methylumbelliferyl-β-D-Glucopyranoside A fluorescent substrate of β-glucosidase and β-glucocerebrosidase

GC40041 Cholesteryl Lignocerate A cholesterol ester

GC40016 Ganglioside GM2 Mixture (sodium salt) A mixture of ganglioside G_M2

GC18609 1-Deoxysphinganine (m18:0) An atypical sphingolipid

GC18469 Galactosylcerebrosides (bovine) A sphingolipid