Search Site
  • 0
    My Cart

    Click Here to Find How Many Items You Have Added:)

qq在线咨询
Home >> Signaling Pathways >> Metabolism >> Inborn Errors of Metabolism

Inborn Errors of Metabolism(先天性代谢缺陷病)

  1. Cat.No. 产品名称 Information
  2. GC52496 Sulfatide (bovine) (sodium salt) A mixture of isolated bovine sulfatides
  3. GC52493 Glucosylceramide (bovine buttermilk) A sphingolipid
  4. GC52492 Globotriaosylceramide (hydroxy) (porcine RBC) A sphingolipid
  5. GC52491 Globotriaosylceramide (non-hydroxy) (porcine RBC) A sphingolipid
  6. GC52404 γ-Glu-Phe (trifluoroacetate salt) A dipeptide with metabolism-altering activity
  7. GC52323 L-Isoleucine-13C6 An internal standard for the quantification of L-isoleucine
  8. GC52231 Heptadecanoyl-L-carnitine-d3 (chloride) An internal standard for the quantification of heptadecanoyl-L-carnitine
  9. GC52219 Heptadecanoyl-L-carnitine (chloride) A long-chain acylcarnitine
  10. GC52122 2’-Deoxyadenosine-5’-diphosphate (sodium salt) A nucleotide diphosphate
  11. GC52083 21-Deoxycortisone A corticosteroid metabolite of 11-keto progesterone
  12. GC52009 Isovaleryl-DL-carnitine-d9 (chloride) An internal standard for the quantification of isovaleryl-DL-carnitine
  13. GC49840 2-Methylbutyrylglycine A metabolite of isoleucine
  14. GC49782 L-Phenylalanine-13C6 An internal standard for the quantification of phenylalanine
  15. GC49678 Heptadecanoyl-L-carnitine-d3 (chloride) MaxSpec® Standard A quantitative analytical standard guaranteed to meet MaxSpec® identity, purity, stability, and concentration specifications
  16. GC49499 5(Z)-Dodecenoic Acid A medium-chain unsaturated fatty acid
  17. GC49479 Hypoxanthine-d4 An internal standard for the quantification of hypoxanthine
  18. GC49472 Methylmalonic Acid-d3 An internal standard for the quantification of methylmalonic acid
  19. GC49388 N-Butyldeoxynojirimycin-d9 (hydrochloride) An internal standard for the quantification of N-butyldeoxynojirimycin
  20. GC49328 UDP-α-D-Galactose (sodium salt) A nucleotide sugar
  21. GC49325 Dihydroxyacetone Phosphate (magnesium salt hydrate) 甘油脂前体
  22. GC49323 Norcholic Acid A bile acid and derivative of cholic acid
  23. GC49246 N-(3-Phenylpropionyl)glycine An acylglycine
  24. GC49240 N-Propionylglycine A glycine-conjugated form of propionic acid
  25. GC49149 3-Methylglutaconic Acid A branched-chain organic acid
  26. GC48724 Pregnanetriol A metabolite of 17α-hydroxyprogesterone
  27. GC47779 Nitisinone-13C6 An internal standard for the quantification of nitisinone
  28. GC47392 Ganglioside GM1 Mixture (ovine) (ammonium salt) A sphingolipid
  29. GC47286 Eliglustat-d15 (tartrate) An internal standard for the quantification of eliglustat
  30. GC47204 D-Fructose-13C6 An internal standard for the quantification of D-fructose
  31. GC47189 D-erythro/L-threo Lysosphingomyelin (d18:1) A mixture of bioactive sphingolipids
  32. GC46735 7-Biopterin A pterin
  33. GC46540 2'-Deoxyadenosine-5'-triphosphate (sodium salt hydrate) A purine nucleotide
  34. GC46243 24-dehydro Cholesterol-d6 An internal standard for the quantification of 24-dehydro cholesterol
  35. GC46242 7-dehydro Cholesterol-d7 An internal standard for the quantification of 7-dehydro cholesterol
  36. GC46215 S-Acetyl-L-glutathione A derivative of glutathione
  37. GC46192 Octanoic Acid-13C An internal standard for the quantification of octanoic acid
  38. GC46187 Norhyodeoxycholic Acid A synthetic bile acid
  39. GC46068 3β-OH-7-Oxocholenic Acid A bile acid
  40. GC45996 Octanoic Acid-d2 An internal standard for the quantification of octanoic acid
  41. GC45982 Octanoic Acid-d15 An internal standard for the quantification of octanoic acid
  42. GC45981 Pristanic Acid-d3

    An internal standard for the quantification of pristanic acid
  43. GC45945 Trihydroxycholestanoic Acid A cholic acid intermediate
  44. GC45813 Octanoic Acid-d3 An internal standard for the quantification of octanoic acid
  45. GC44968 Sulfatides (bovine) (sodium salt) Sulfatides are endogenous sulfoglycolipids with various biological activities in the central and peripheral nervous systems, pancreas, and immune system.
  46. GC44488 Octanoyl Coenzyme A (sodium salt) A medium-chain acyl CoA
  47. GC44105 Lysosphingomyelin (d18:1) A bioactive sphingolipid
  48. GC44101 Lyso-Globotriaosylceramide (d18:1) A globotriaosylceramide lacking the fatty acyl group
  49. GC43914 Isobutyryl Coenzyme A (sodium salt) A short-chain branched acyl CoA
  50. GC43768 Glucocerebrosides (Gaucher's spleen) A sphingolipid
  51. GC43760 Globotriaosylceramides (porcine) A sphingolipid

Items 1 to 50 of 80 total

per page
  1. 1
  2. 2

Set Descending Direction